E76.0

Mukopolysaccharidose, Typ I
Inclusions
  • Hurler-Scheie-Variante
  • Pfaundler-Hurler-Krankheit
  • Scheie-Krankheit
Exclusions
  • -
Synonyms
  • Hurler-Scheie-Syndrom
  • Hurler-Scheie-Krankheit
  • Alpha-L-Iduronidase-Mangel
  • Gargoylismus
  • Hurler-Scheie-Variante [Mukopolysaccharidose Typ I-H/S]
  • Enchondrale Dysostose
  • Mukopolysaccharidose Typ I-S
  • Dysostotische Idiotie [Pfaundler-Hurler-Syndrom]
  • Von-Pfaundler-Hurler-Syndrom
  • Hurler-Krankheit
  • Von-Pfaundler-Hurler-Krankheit
  • Mukopolysaccharidose Typ I
  • Hurler-Syndrom
  • Dysostosis multiplex
  • MPS I [Mukopolysaccharidose Typ I]
  • Lipochondrodystrophie
  • Scheie-Syndrom
Coding hint
-
Note
-
Sub-codes
  • -
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